Congenital corrected transposition of the great arteries manifesting in adult: A classic case

Thawanan Wongpen; Warit Tarathipmon; Amolchaya Kwankua; Wanrudee Lohitvisate; massupa krisem

doi:10.46475/asean-jr.v27i3.978

Authors

Thawanan Wongpen, M.D. Department of Radiology, Faculty of Medicine, Thammasat University Hospital, Pathum Thani, Thailand.
Warit Tarathipmon, M.D. Department of Radiology, Faculty of Medicine, Thammasat University Hospital, Pathum Thani, Thailand.
Amolchaya Kwankua, M.D. Department of Radiology, Faculty of Medicine, Thammasat University Hospital, Pathum Thani, Thailand.
Wanrudee Lohitvisate, M.D. Department of Radiology, Faculty of Medicine, Thammasat University Hospital, Pathum Thani, Thailand.
Massupa Krisem, M.D. Department of Radiology, Faculty of Medicine, Thammasat University Hospital, Pathum Thani, Thailand.

DOI:

https://doi.org/10.46475/asean-jr.v27i3.978

Keywords:

Congenitally Corrected Transposition of the Great Arteries (CCTGA), Dextrocardia, Heart Failure, Multimodality Cardiac Imaging, Systemic Right Ventricle

Abstract

Congenitally corrected transposition of the great arteries (CCTGA) is a rare congenital

anomaly characterized by atrioventricular and ventriculoarterial discordance, in

which the morphologic right ventricle supports systemic circulation, often leading

to progressive dysfunction and heart failure in adulthood. We report the case of a

33-year-old man presenting with progressively worsening dyspnea. Chest radiography

demonstrated cardiomegaly with dextrocardia and features of pulmonary interstitial

edema. Multimodality imaging—including transthoracic echocardiography, coronary CT

angiography, and cardiac MRI—was essential in confirming CCTGA and assessing secondary

right ventricular failure. This case highlights the critical role of early recognition

and comprehensive imaging in guiding management and optimizing outcomes in

adult patients with this rare congenital condition.

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