Hemophilic pseudotumor of the skull: A rare presentation in a young child
DOI:
https://doi.org/10.46475/asean-jr.v26i3.937Keywords:
Hemophilia, Hemophilic pseudotumor, Scalp, SkullAbstract
Hemophilic pseudotumors are rare complications of severe hemophilia and typically involve muscles and bones. We present the case of a 1-year-old 5-month-old boy with severe hemophilia A, who developed progressively enlarging left occipital scalp swelling. A computed tomography (CT) scan revealed a significant left occipital osteolytic calvarial mass causing a mass effect and displacing the 4th ventricle. The absence of acute neurological compromise allowed for conservative management in this case. This case highlights the importance of considering hemophilic pseudotumors in patients with hemophilia, even in atypical locations. Early recognition and individualized management are crucial for optimal outcomes in patients with this challenging complication.
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