HYDRANENCEPHALY : CASE REPORT AND LITERATURE REVIEW
Abstract
Hydranencephaly is the total or virtually total absence of the cerebral hemispheres, which are reduced to membranous sac of glia tissue, with no ependymal coating, in an intact skull. This is rare disorder. It is classified as a circulatory encephalopathy from many causes (vascular, parasitic, viral,toxic,estrogenic,...).
It appears to be readily diagnoses prenatal by ultrasound. The neurological findings may be normal at birth. Transfrontanellar ultrasound,CT scanning and anatomical confirmation can established the diagnosis. The prognosis is hopeless and there is no treatment. Our report presents one case of hydranencephaly, clinical presentation and differential diagnosis from other common congenital diseases.
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