US AND CT OF CAROLI DISEASE: REPORT OF TWO CASES

Authors

  • Pannee VISRUTARATNA Department of Radiology
  • Sukanya REUNGRONGRAT Department of Radiology
  • Lumdaun WONGSAWASDI Department of Pediatrics
  • Aumnart YOUSUKH Department of Pathology. Faculty of Medicine, Chiang Mai University

Abstract

Caroli disease is a rare congenital disorder with multiple cystic dilatation of the intrahepatic bile ducts. We report two pediatric patients with cystic dilatation of intrahepatic bile ducts accompanying congenital hepatic fibrosis. CT scans of the liver showed tiny dots with strong contrast enhancement inside dilated intrahepatic bile ducts ("central dot signs"). These dot signs in CT scans corresponded to intraluminal portal veins in sonograms. Ultrasonography and CT scans are very effective noninvasive methods to diagnose this disease.

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References

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Published

2023-04-07

How to Cite

1.
VISRUTARATNA P, REUNGRONGRAT S, WONGSAWASDI L, YOUSUKH A. US AND CT OF CAROLI DISEASE: REPORT OF TWO CASES. ASEAN J Radiol [Internet]. 2023 Apr. 7 [cited 2024 May 13];3(3):257-62. Available from: https://asean-journal-radiology.org/index.php/ajr/article/view/396

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