Imaging Findings of OHVIRA Syndrome with Surgical Correlation in an 11-Year-Old Girl: A classic case

Fon Suratsukkasem

doi:10.46475/asean-jr.v27i2.1021

Authors

Fon Suratsukkasem, M.D. Department of Radiology, Mahidol Bumrungrak Nakhonsawan Medical Center, Nakhonsawan, Thailand.

DOI:

https://doi.org/10.46475/asean-jr.v27i2.1021

Keywords:

OHVIRA syndrome, Obstructed hemivagina, Renal agenesis, Ultrasound, Computed tomography

Abstract

OHVIRA syndrome (Obstructed Hemivagina and Ipsilateral Renal Agenesis) is a rare congenital Müllerian duct anomaly characterized by uterine duplication, obstructed hemivagina, and ipsilateral renal agenesis. Early recognition is essential to prevent long-term complications such as endometriosis and infertility. We report the case of an 11-year-old girl who presented with acute lower abdominal pain for one day without fever. Physical examination revealed a 10-cm vaginal mass. Transabdominal ultrasonography demonstrated a cystic mass in the mid-pelvic cavity. Contrast-enhanced computed tomography confirmed uterine didelphys with marked distension of the right hemivagina and absence of the right kidney. Surgical exploration revealed a bulging right hemivagina with approximately 400 mL of retained brownish fluid, and vaginal septum excision was performed. The postoperative course was uneventful. This case highlights the importance of multimodality imaging in the early diagnosis and management of OHVIRA syndrome.

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